改良尺骨逐步延长法治疗遗传性多发性骨软骨瘤引发的Masada Ⅰ型前臂畸形的疗效

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Abstract Objective To investigate the clinical effect of modified gradual ulnar lengthening in the treatment of Masada type I forearm deformity caused by hereditary multiple osteochondroma. Methods A total of 10 (11 limbs) patients with Masada type I forearm deformity caused by hereditary multiple osteochondroma were treated at the Department of Orthopedics of Beijing Children's Hospital affiliated to Capital Medical University from June 2014 to October 2020. The patients, 8 males and 2 females, were (10.0±2.8) years old. The clinical and imaging data were retrospectively analyzed, and the radial articular articular angle (RAA), carpal slip (CS), relative ulna shortening (RUS) were compared before and after surgery. The flexion and extension range of wrist, the ulnar deviation and radial deviation of wrist, the pronation and supination range of forearm and the flexion and extension range of elbow were evaluated. Results The mean follow-up was (38.2±6.6) months, and the mean length of the ulna was (38.9±6.6) mm. There were no statistically significant differences between preoperative and last follow-up in RAA[(40.1°±14.2°) vs. (39.3°±13.8°)], supination of forearm [(48.2°±7.5°) vs. (53.6°±6.0°)], elbow range of motion [(135.5°±3.5°) vs. (136.8°±3.4°)], (P＞0.05). There were significant differences between post-operative and last follow-up in CS [(65.0%±22.5%) vs. (34.1%±10.4%)], RUS [(11.2±2.2)mm vs. (-3.9±5.3)mm], wrist flexion [(40.0°±7.7°) vs. (54.5°±7.9°)], wrist extension [(45.9°±8.6°) vs. (61.4°±6.4°)], ulnar deviation [(42.7°±7.5°) vs. (30.5°±6.5°)], radial deviation [(17.7°±4.7°) vs. (29.1±4.9°)] and pronation of forearm [(59.1°±5.4°) vs. (65.0°±3.9°)], (P<0.05). Pathological fracture occurred in 1 case during follow-up. Conclusions Modified gradual ulnar lengthening can effectively treat Masada type I forearm deformity caused by hereditary multiple osteochondroma and improve forearm function.

Key words： modified gradual ulnar lengthening hereditary multiple osteochondroma forearm deformity Masada type Ⅰ

Received: 13 February 2023

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	Articles by authors
	FAN Jingyi
	ZHANG Xuejun
	SUN Lin
	LI Chengxin
	QI Xinyu
	SUN Baosheng

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FAN Jingyi,ZHANG Xuejun,SUN Lin等. Modified gradual ulnar lengthening in treatment of Masada type I forearm deformity caused by hereditary multiple osteochondroma[J]. Med. J. Chin. Peop. Armed Poli. Forc., 2023, 34(7): 572-576.

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http://journal08.magtechjournal.com/Jwk_wjyx/EN/ OR http://journal08.magtechjournal.com/Jwk_wjyx/EN/Y2023/V34/I7/572

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